Disease

X-linked Lymphoproliferative Disease, LPD

About the Disease
Lymphoproliferative Syndrome, X-Linked, 1, also known as lymphomatoid papulosis, is related to primary cutaneous anaplastic large cell lymphoma and lymphoproliferative syndrome, x-linked, 2. An important gene associated with Lymphoproliferative Syndrome, X-Linked, 1 is SH2D1A (SH2 Domain Containing 1A), and among its related pathways/superpathways are Signal Transduction and Akt Signaling. The drugs Cytarabine and Lenalidomide have been mentioned in the context of this disorder. Affiliated tissues include skin, t cells and bone marrow, and related phenotypes are fever and cervical lymphadenopathy

Common Targets
XIAP | DGKA | SH2D1A

疾病靶点研报
X-linked Lymphoproliferative Disease, LPD

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